I went to him. (and there is also a member who is no longer active, Lovelily, who went to him)
His specialty is myasthenia gravis, but, he has experience in the neuromuscular field that goes beyond just MG. I would definitely not completely discount what he has to say, but, he is known to have a bit of an ego as far as liking to contradict what other neurologists have diagnosed.
I would take it as a sign you need to continue investigating other possible causes. But (IMO) I would not count on it being him that discovers what is wrong with you if its not ALS.
When I saw him, he was the neurologist who performed the EMG on my vocal cords (with my laryngologist, she did the needle work, he and another specialist interpreted the readings as the test was performed) When the test was abnormal, and the findings were indicative of either MND or myasthenia gravis, he halted the test, even though my laryngologist (an ENT) wanted to continue with tensilon to see what result it would have. He was adamant that I did not have myasthenia, despite it being the first time he had ever met me, no exam, etc. My larygnologist brought me out into the hallway to discuss my results, and she was frustrated that he would not continue the testing looking for more signs it could be mysathenia. At the time I did not understand the significance of why she wanted it to be MG, because no one had actually broached the subject of ALS with me, and any form of MND was completely off of my radar. I was actually relieved that testing had finally turned something up. Back then I didn't really understand what the EMG was testing for. "Chronic and active denervation and reinnervation" meant nothing to me.
I remember she ordered blood labs for MG even though he said they were not necessary because he "knew" I didn't have it.
SO, that was my experience with him. (and later testing did prove that I don't have MG, so he was right, but that's beside the point in a way)
He does not have a terrific manner in how he interacts with patients, and can seem arrogant and quick to judge, but he is good, is not incompetent, at least not in my estimation.
I know I've suggested it before, but, please consider going down to Johns Hopkins.