Help with diagnosis

[sassy]

What criteria is used to differentiate between limb onset and flail leg. Is progression or lack of it the only measure?

As always, thanks for your help.

 

[KarenNWendyn]

My understanding (and others please correct me if I’m wrong) is that flail leg is a primarily LMN disease involving one or both legs, starting distally, and with very slow progression. Lifespan and prognosis of this is better than average for ALS, but I believe most of these gradually evolve into ALS and acquire UMN findings over time.

What I don’t know is whether or not EMG in areas other than the affected leg(s) would show abnormalities right away. I suspect it would eventually as the disease progresses.

 

[sassy]

Thanks Karen. I think I posted my question in the wrong place. My husband has already been diagnosed and his progression is thankfully slow so I was just trying to gather some info before his next clinic visit.